| Rheumatic Disease | Ophthalmic Manifestations |
| Sjögren Syndrome | Keratitis sicca |
| Adult Rheumatoid Arthritis | Keratitis sicca, Scleritis |
| Relapsing Polychondritis | Scleritis, Orbital pseudotumor |
| Granulomatous Polyangiitis (Wegener Granulomatosis) | Scleritis, Sclerokeratitis, Orbital pseudotumor |
| Reiter Syndrome | Uveitis, Conjunctivitis |
| Behçet Disease | Uveitis, Retinal vascular occlusion |
| Juvenile Pauciarticular Arthritis | Uveitis |
| Sarcoidosis | Uveitis, Retinal vascular occlusion |
| Ankylosing Spondylitis | Uveitis |
| Lupus Erythematosus | Retinal vascular occlusion |
| Polyarteritis Nodosa | Retinal vascular occlusion |
| Scleroderma | Retinal vascular occlusion, Keratitis sicca |
| Primary CNS Angiitis | Retinal vascular occlusion |
| Giant Cell Arteritis | Ischemic optic neuropathy |